2. Gene
  3. Mccc1 - methylcrotonyl-CoA carboxylase subunit 1 Gene

Mccc1 - methylcrotonyl-CoA carboxylase subunit 1 Gene

  • Gene
  • Protein
  • Agent
  • Ortholog
Rattus norvegicus
Gene ID: 294972 | Gene type: protein coding

About Mccc1

Summary

Predicted to enable ATP binding activity and metal ion binding activity. Predicted to contribute to methylcrotonoyl-CoA carboxylase activity. Predicted to be involved in leucine catabolic process. Predicted to be located in mitochondrial matrix. Predicted to be part of methylcrotonoyl-CoA carboxylase complex. Predicted to be active in mitochondrion. Human ortholog(s) of this gene implicated in 3-Methylcrotonyl-CoA carboxylase 1 deficiency. Orthologous to human MCCC1 (methylcrotonyl-CoA carboxylase subunit 1). [provided by Alliance of Genome Resources, Apr 2022]

Mccc1 Products(1)

mRNA Protein Name
NM_001009653.1 NP_001009653.1 methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
Protein Preferred Names Protein Names

methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial

3-methylcrotonyl-CoA carboxylase 1

3-methylcrotonyl-CoA carboxylase biotin-containing subunit

3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha

MCCase subunit alpha

methylcrotonoyl-CoA carboxylase 1 (alpha)

methylcrotonoyl-Coenzyme A carboxyla

Related Agents

Pre-clinical Phase
Bioactive Molecules (2)
Cat. No. Product Name Effect
Purity Rare Diseases
HY-170692 Hypoglycemic agent 3 / Unkown
HY-RS08218 MCCC1 Human Pre-designed siRNA Set A Pre-designed Set / Unkown

Orthologs Information

Species Symbol Source ID
Homo sapiens Mccc1 NCBI NCBI:56922