1. Gene
  2. BCKDHB - branched chain keto acid dehydrogenase E1 subunit beta Gene

BCKDHB - branched chain keto acid dehydrogenase E1 subunit beta Gene

Bos taurus
Gene ID: 282150 | Gene type: protein coding

About BCKDHB

BCKDHB Products(1)

mRNA Protein Name
NM_174507.2 NP_776932.1 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial precursor
Protein Preferred Names Protein Names

2-oxoisovalerate dehydrogenase subunit beta, mitochondrial

BCKDE1B

BCKDH E1-beta

branched chain keto acid dehydrogenase E1, beta polypeptide (maple syrup urine disease)

branched-chain alpha-keto acid dehydrogenase E1 component beta chain

Orthologs Information

Species Symbol Source ID
Homo sapiens BCKDHB NCBI NCBI:594