1. Gene
  2. BCKDHA - branched chain keto acid dehydrogenase E1 subunit alpha Gene

BCKDHA - branched chain keto acid dehydrogenase E1 subunit alpha Gene

Bos taurus
Gene ID: 282149 | Gene type: protein coding

About BCKDHA

BCKDHA Products(1)

mRNA Protein Name
NM_174506.1 NP_776931.1 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial precursor
Protein Preferred Names Protein Names

2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial

BCKDE1A

BCKDH E1-alpha

branched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease)

branched-chain alpha-keto acid dehydrogenase E1 component alpha chain

Orthologs Information

Species Symbol Source ID
Homo sapiens BCKDHA NCBI NCBI:593