BCKDHA - branched chain keto acid dehydrogenase E1 subunit alpha Gene

Species: Bos taurus

Gene Type: protein coding
Gene ID: 282149

BCKDHA Products (1)

mRNA Protein Name
NM_174506.1 NP_776931.1 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial precursor
Protein Preferred Names Protein Names

2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial

  • BCKDE1A

  • BCKDH E1-alpha

  • branched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease)

  • branched-chain alpha-keto acid dehydrogenase E1 component alpha chain

Orthologs Information

Species Symbol Source ID
Homo sapiens BCKDHA NCBI NCBI:593