1. Gene
  2. Mccc1 - methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) Gene

Mccc1 - methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) Gene

Mus musculus

Also known as Mcca; MCCalpha; 1810045E08Rik; 2310058B18Rik

Gene ID: 72039 | Gene type: protein coding

About Mccc1

Summary

Predicted to enable ATP binding activity; Ligase activity; and metal ion binding activity. Predicted to contribute to methylcrotonoyl-CoA carboxylase activity. Located in mitochondrial inner membrane. Is expressed in several structures, including alimentary system; genitourinary system; heart; nervous system; and sensory organ. Human ortholog(s) of this gene implicated in 3-Methylcrotonyl-CoA carboxylase 1 deficiency. Orthologous to human MCCC1 (methylcrotonyl-CoA carboxylase subunit 1). [provided by Alliance of Genome Resources, Apr 2022]

Mccc1 Products(1)

mRNA Protein Name
NM_023644.4 NP_076133.3 methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
Protein Preferred Names Protein Names

methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial

3-methylcrotonyl-CoA carboxylase 1

3-methylcrotonyl-CoA carboxylase biotin-containing subunit

3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha

MCCase subunit alpha

Orthologs Information

Species Symbol Source ID
Homo sapiens Mccc1 NCBI NCBI:56922