4 Results for "

type II glycogen storage disease

" in MedChemExpress (MCE) Product Catalog:
Products (4)

4 Results for "type II glycogen storage disease" in MCE Product Catalog:

Cat. No.: HY-P2857
CAS No.: 9032-08-0
Synonyms: Amyloglucosidase, Aspergillus niger
Amyloglucosidase, Aspergillus niger (Amyloglucosidase, Aspergillus niger) is a starch-hydrolyzing enzyme with high catalytic efficiency towards soluble starch and raw starch. Amyloglucosidase, Aspergillus niger hydrolyzes α-1,4 and α-1,6 glycosidic linkages in starch and similar substrates, and primarily releases β-glucose molecules from the non-reducing ends. Amyloglucosidase, Aspergillus niger participates in glycogen metabolism and is associated with type II glycogen storage disease. Amyloglucosidase, Aspergillus niger converts starch into glucose, and is applicable to the industrial production of high-fructose syrup, ethanol and other fermented products .
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Cat. No.: HY-P2857A
CAS No.: 9032-08-0
Synonyms: Amyloglucosidase, Rhizopus sp.
Target:  

Glycosidase

Research Areas:  

Metabolic Disease

Glucoamylase, Rhizopus sp. (Amyloglucosidase, Rhizopus sp.) is a starch-hydrolyzing enzyme with high catalytic efficiency towards soluble starch and raw starch. Glucoamylase, Rhizopus sp. hydrolyzes α-1,4 and α-1,6 glycosidic linkages in starch and similar substrates, and primarily releases β-glucose molecules from the non-reducing ends. Glucoamylase, Rhizopus sp. participates in glycogen metabolism and is associated with type II glycogen storage disease. Glucoamylase, Rhizopus sp. converts starch into glucose, and is applicable to the industrial production of high-fructose syrup, ethanol and other fermented products .
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Cat. No.: HY-E70183
Synonyms: EC:3.2.1.20; GAA
Lysosomal α-Glucosidase (EC:3.2.1.20) is a lysosomal α-Glucosidase that degrades glycogen into glucose and catalyzes the hydrolysis of α-1,4 and α-1,6 glycosidic linkages in glycogen, as well as that of natural and synthetic oligoglucosides. Deficiency of Lysosomal α-Glucosidase causes type II glycogen storage disease (Pompe disease), which is characterized by lysosomal glycogen accumulation in mammals and birds. Lysosomal α-Glucosidase can be used in research related to type II glycogen storage disease .
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Cat. No.: HY-P810401
Synonyms: 70 kDa lysosomal alpha-glucosidase, Acid alpha glucosidase, Acid maltase, Aglucosidase alfa, Alpha glucosidase, GAA, Glucosidase alpha acid (Pompe disease glycogen storage disease type II), Glucosidase alpha acid, Glucosidase alpha, LYAG

Host:  

Rabbit

Application:  

WB, IF-Tissue, IHC-P

Reactivity:  

Human

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