1 Result for "

Succinyl CoA disodium

" in MedChemExpress (MCE) Product Catalog:
Products (1)

1 Results for "Succinyl CoA disodium" in MCE Product Catalog:

Cat. No.: HY-148285A
CAS No.: 403982-65-0
Synonyms: Succinyl-coenzyme A disodium; S-(Hydrogen Succinyl)coenzyme A disodium
Target:  

Endogenous Metabolite

Research Areas:  

Metabolic Disease

Succinyl CoA (Succinyl-coenzyme A) disodium is a pivotal intermediate metabolite in the tricarboxylic acid cycle and a key coenzyme A metabolite. Succinyl CoA disodium is biosynthesized from α-ketoglutarate or propionyl-CoA. Succinyl CoA disodium acts as a critical precursor and substrate for heme biosynthesis and gluconeogenesis. Succinyl CoA disodium insufficiency caused by cobalamin deficiency is directly linked to growth retardation, impaired heme synthesis, tissue glycine accumulation and neurological abnormalities. Succinyl-Coenzyme A sodium can be used in research on metabolic, neurological, and hematological abnormalities (such as porphyria) caused by nutritional vitamin B12 deficiency (leading to a lack of Succinyl-Coenzyme A synthesis) .
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