2636-52-4
2636-52-4
Chemical Structure
L-Primapterin
Synonym(s): 7-Biopterin
- CAS No.: 2636-52-4
- Formula:C9H11N5O3
- Molecular Weight:237.22
IUPAC Name: 2-amino-7-((1R,2S)-1,2-dihydroxypropyl)pteridin-4(8H)-one
InChIKey: LNXRKRFGNHXANN-DZSWIPIPSA-N
SMILES: O=C1C2=NC=C([C@@H](O)[C@@H](O)C)NC2=NC(N)=N1
Biological Activity: L-Primapterin (7-Biopterin) is the 7-isomer of L-biopterin. L-Primapterin is a characteristic marker of hyperphenylalaninemia variant primapterinuria, which is excreted in the urine[1][2].
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L-Primapterin | L-Primapterin (7-Biopterin) is the 7-isomer of L-biopterin. L-Primapterin is a characteristic marker of hyperphenylalaninemia variant primapterinuria, which is excreted in the urine. | |||||||||||||||||||||
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References
- [1]. Curtius HC, et al. Progress in the study of biosynthesis and role of 7-substituted pterins: function of pterin-4a-carbinolamine dehydratase. Adv Exp Med Biol. 1993;338:107-10. [Content Brief]
- [2]. Ayling JE, et al. Hyperphenylalaninemia and 7-pterin excretion associated with mutations in 4a-hydroxy-tetrahydrobiopterin dehydratase/DCoH: analysis of enzyme activity in intestinal biopsies. Mol Genet Metab. 2000 Jul;70(3):179-88. [Content Brief]
