8 Results for "

medium-chain acyl-coa dehydrogenase deficiency

" in MedChemExpress (MCE) Product Catalog:
Products (8)

8 Results for "medium-chain acyl-coa dehydrogenase deficiency" in MCE Product Catalog:

1
1 Cited Publications
Cat. No.: HY-W014787
CAS No.: 111-20-6
Synonyms: Sebacic acid
Decanedioic acid is a straight-chain dicarboxylic acid. Dodecanedioic acid overcomes metabolic inflexibility in type 2 diabetes. Decanedioic acid prevents and reverses metabolic-associated liver disease and obesity. Decanedioic acid is associated with carnitine-acylcarnitine translocase deficiency and medium chain acyl-CoA dehydrogenase deficiency .
loading...
    loading...
Cat. No.: HY-115703
CAS No.: 67492-16-4
Synonyms: N-Heptadecanoyl-D-erythro-sphingosine
Research Areas:  

Metabolic Disease

C17 Ceramide (d18:1/17:0) (N-Heptadecanoyl-D-erythro-sphingosine) is a phospholipid internal standard. C17 Ceramide (d18:1/17:0) is used in studies of medium-chain acyl-CoA dehydrogenase deficiency (MCADD) .
loading...
    loading...
Cat. No.: HY-113406
CAS No.: 6418-78-6
Synonyms: DL-Hexanoylcarnitine
(±)-Hexanoylcarnitine exists in human urine and plasma. (±)-Hexanoylcarnitine can be used as a plasma detection indicator in patients with methylmalonic aciduria, propionic acidemia, and medium-chain acyl-CoA dehydrogenase deficiency .
loading...
    loading...
Cat. No.: HY-148869
CAS No.: 5060-32-2
Synonyms: R-Hexanoyl-coa; R-Hexanoyl coenzyme A
Hexanoyl coenzyme A is a short-chain fatty acyl-CoA thioester. Hexanoyl coenzyme A competes with butyryl-CoA to abolish the dehydrogenation effect of medium-chain acyl-CoA dehydrogenase on butyryl-CoA, and does not serve as a substrate for short-chain acyl-CoA dehydrogenase. Hexanoyl coenzyme A acts as a biosynthetic precursor for the synthesis of olivetolic acid and cannabinoids. Hexanoyl coenzyme A is applicable to research related to short-chain acyl-CoA dehydrogenase deficiency .
loading...
    loading...
Cat. No.: HY-W014787R
CAS No.: 111-20-6
Synonyms: Sebacic acid (Standard)
Decanedioic acid (Standard) is the analytical standard of Decanedioic acid (HY-W014787). This product is intended for research and analytical applications. Decanedioic acid is a straight-chain dicarboxylic acid. Dodecanedioic acid overcomes metabolic inflexibility in type 2 diabetes. Decanedioic acid prevents and reverses metabolic-associated liver disease and obesity. Decanedioic acid is associated with carnitine-acylcarnitine translocase deficiency and medium chain acyl-CoA dehydrogenase deficiency .
loading...
    loading...
Cat. No.: HY-W014787S
CAS No.: 339080-77-2
Decanedioic acid-d4 is the deuterium labeled Decanedioic acid (HY-W014787). Decanedioic acid is a straight-chain dicarboxylic acid. Dodecanedioic acid overcomes metabolic inflexibility in type 2 diabetes. Decanedioic acid prevents and reverses metabolic-associated liver disease and obesity. Decanedioic acid is associated with carnitine-acylcarnitine translocase deficiency and medium chain acyl-CoA dehydrogenase deficiency .
loading...
    loading...
Cat. No.: HY-W014787S1
CAS No.: 73351-71-0
Decanedioic acid-d16 is the deuterated-labeled Decanedioic acid (HY-W014787). Decanedioic acid is a straight-chain dicarboxylic acid. Dodecanedioic acid overcomes metabolic inflexibility in type 2 diabetes. Decanedioic acid prevents and reverses metabolic-associated liver disease and obesity. Decanedioic acid is associated with carnitine-acylcarnitine translocase deficiency and medium chain acyl-CoA dehydrogenase deficiency .
loading...
    loading...
Cat. No.: HY-W014787S2
Synonyms: Sebacic acid-13C2
Decanedioic acid- 13C2 (Sebacic acid- 13C2) is the 13C-labeled Decanedioic acid (HY-W014787). Decanedioic acid is a straight-chain dicarboxylic acid. Dodecanedioic acid overcomes metabolic inflexibility in type 2 diabetes. Decanedioic acid prevents and reverses metabolic-associated liver disease and obesity. Decanedioic acid is associated with carnitine-acylcarnitine translocase deficiency and medium chain acyl-CoA dehydrogenase deficiency .
loading...
    loading...