3-Hydroxyisovalerylcarnitine (Standard)

3-Hydroxyisovalerylcarnitine (Standard) is the analytical standard of 3-Hydroxyisovalerylcarnitine. This product is intended for research and analytical applications. 3-Hydroxyisovalerylcarnitine is a carnitine derivative. 3-Hydroxyisovaleryl carnitine in plasma may serve as a novel biomarker of biotin deficiency in humans, with its concentration increasing with biotin deficiency. Biotin deficiency reduces the activity of biotin-dependent 3-methylcrotonyl-CoA carboxylase, hinders the conversion of 3-methylcrotonyl-CoA into 3-methylglutaconyl-CoA, and impairs the leucine catabolism pathway; resulting in plasma 3-Hydroxyisovalerylcarnitine concentrations rise.

For research use only. We do not sell to patients.

  • CAS No.: 99159-87-2
  • Formula: C12H23NO5
  • Molecular Weight:261.31
  • Storage:

    Please store the product under the recommended conditions in the Certificate of Analysis.

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100 mg

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