SOD1 - superoxide dismutase 1 Gene
Also Known as ALS; SOD; ALS1; IPOA; STAHP; hSod1; HEL-S-44; homodimer
Species: Homo sapiens
About SOD1
This gene has 4 transcripts (splice variants), 229 orthologues, 2 paralogues and is associated with 3 phenotypes. Ubiquitous expression in liver (RPKM 426.2), kidney (RPKM 226.6) and 23 other tissues.
Summary
The protein encoded by this gene binds copper and zinc ions and is one of two isozymes responsible for destroying free superoxide radicals in the body. The encoded isozyme is a soluble cytoplasmic protein, acting as a homodimer to convert naturally-occuring but harmful superoxide radicals to molecular oxygen and hydrogen peroxide. The Other isozyme is a mitochondrial protein. In addition, this protein contains an antimicrobial peptide that displays Antibacterial, Antifungal, and anti-MRSA activity against E. coli, E. faecalis, S. aureus, S. aureus MRSA LPV+, S. agalactiae, and yeast C. krusei. Mutations in this gene have been implicated as causes of familial amyotrophic lateral sclerosis. Rare transcript variants have been reported for this gene. [provided by RefSeq, Jul 2020]
SOD1 Products (1)
| mRNA | Protein | Name |
|---|---|---|
| NM_000454.5 | NP_000445.1 | superoxide dismutase [Cu-Zn] |
| Molecular Function GO Annotation | Evidence | References | Source |
|---|---|---|---|
| enables copper ion binding |
IDA
IDA: Inferred from direct assay
|
17008312 | GOA |
| enables identical protein binding |
IPI
IPI: Inferred from physical interaction
|
17592131 | GOA |
| enables protein binding |
IPI
IPI: Inferred from physical interaction
|
12968035 | GOA |
| enables protein homodimerization activity |
IPI
IPI: Inferred from physical interaction
|
24567322 | GOA |
| enables protein phosphatase 2B binding |
IDA
IDA: Inferred from direct assay
|
17324120 | GOA |
| enables protein-folding chaperone binding |
IPI
IPI: Inferred from physical interaction
|
9726962 | GOA |
| enables small GTPase binding |
IDA
IDA: Inferred from direct assay
|
18219391 | GOA |
| enables superoxide dismutase activity |
IDA
IDA: Inferred from direct assay
|
12551919 | GOA |
| enables zinc ion binding |
IDA
IDA: Inferred from direct assay
|
17381088 | GOA |
| Cellular Component GO Annotation | Evidence | References | Source |
|---|---|---|---|
| located in cytoplasm |
IDA
IDA: Inferred from direct assay
|
1332049 | GOA |
| located in cytoplasmic vesicle |
IDA
IDA: Inferred from direct assay
|
17077646 | GOA |
| located in cytosol |
IDA
IDA: Inferred from direct assay
|
16790527 | GOA |
| located in dendrite cytoplasm |
IDA
IDA: Inferred from direct assay
|
17324120 | GOA |
| located in extracellular space |
IDA
IDA: Inferred from direct assay
|
9453566 | GOA |
| located in mitochondrion |
IDA
IDA: Inferred from direct assay
|
16790527 | GOA |
| located in neuronal cell body |
IDA
IDA: Inferred from direct assay
|
17324120 | GOA |
| located in nucleus |
IDA
IDA: Inferred from direct assay
|
1332049 | GOA |
| located in peroxisome |
IDA
IDA: Inferred from direct assay
|
1332049 | GOA |
| colocalizes with plasma membrane |
IDA
IDA: Inferred from direct assay
|
17077646 | GOA |
| part of protein-containing complex |
IDA
IDA: Inferred from direct assay
|
17324120 | GOA |
SOD1 Protein Structure
Sod_Cu: Copper/zinc superoxide dismutase (SODC) (5 - 150)
- 0
- 100
- 154 a.a.
| Protein Preferred Names | Protein Names | |
|---|---|---|
|
superoxide dismutase [Cu-Zn] |
|
SOD1 Protein-protein interaction Information
|
Type
|
Protein Name | Protein ID | Interactor | Interactor Species | Interactor ID | Detection Method | References |
|---|---|---|---|---|---|---|---|
|
Intra
|
SOD1 | P00441 | SGSM1 | Homo sapiens | Q2NKQ1-4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SGSM1 | Homo sapiens | Q2NKQ1-4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SGSM1 | Homo sapiens | Q2NKQ1-4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ARL16 | Homo sapiens | Q0P5N6 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ARL16 | Homo sapiens | Q0P5N6 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ARL16 | Homo sapiens | Q0P5N6 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PBX4 | Homo sapiens | Q9BYU1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PBX4 | Homo sapiens | Q9BYU1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PBX4 | Homo sapiens | Q9BYU1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TMX1 | Homo sapiens | Q9H3N1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TMX1 | Homo sapiens | Q9H3N1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TMX1 | Homo sapiens | Q9H3N1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | OTUB1 | Homo sapiens | Q96FW1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | OTUB1 | Homo sapiens | Q96FW1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | OTUB1 | Homo sapiens | Q96FW1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | C6orf141 | Homo sapiens | Q5SZD1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | C6orf141 | Homo sapiens | Q5SZD1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | C6orf141 | Homo sapiens | Q5SZD1 | 32814053 | |
|
Intra
|
SOD1 | P00441 | KLHL36 | Homo sapiens | Q8N4N3-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | KLHL36 | Homo sapiens | Q8N4N3-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | KLHL36 | Homo sapiens | Q8N4N3-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TPM2 | Homo sapiens | P07951-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TPM2 | Homo sapiens | P07951-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TPM2 | Homo sapiens | P07951-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | LDHAL6B | Homo sapiens | Q9BYZ2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | LDHAL6B | Homo sapiens | Q9BYZ2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | LDHAL6B | Homo sapiens | Q9BYZ2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SP6 | Homo sapiens | Q3SY56 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SP6 | Homo sapiens | Q3SY56 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SP6 | Homo sapiens | Q3SY56 | 32814053 | |
|
Intra
|
SOD1 | P00441 | AP2B1 | Homo sapiens | P63010-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | AP2B1 | Homo sapiens | P63010-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | AP2B1 | Homo sapiens | P63010-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CCS | Homo sapiens | O14618 | 33961781 | |
|
Intra
|
SOD1 | P00441 | CCS | Homo sapiens | O14618 | 24981860 | |
|
Intra
|
SOD1 | P00441 | CCS | Homo sapiens | O14618 | 28514442 | |
|
Intra
|
SOD1 | P00441 | DAB2 | Homo sapiens | P98082 | 32814053 | |
|
Intra
|
SOD1 | P00441 | DAB2 | Homo sapiens | P98082 | 32814053 | |
|
Intra
|
SOD1 | P00441 | DAB2 | Homo sapiens | P98082 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PPP3CA | Homo sapiens | Q08209-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PPP3CA | Homo sapiens | Q08209-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PPP3CA | Homo sapiens | Q08209-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | L3MBTL3 | Homo sapiens | Q96JM7-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | L3MBTL3 | Homo sapiens | Q96JM7-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | L3MBTL3 | Homo sapiens | Q96JM7-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ZSCAN1 | Homo sapiens | Q8NBB4-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ZSCAN1 | Homo sapiens | Q8NBB4-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ZSCAN1 | Homo sapiens | Q8NBB4-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | IFI35 | Homo sapiens | P80217-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | IFI35 | Homo sapiens | P80217-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | IFI35 | Homo sapiens | P80217-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RNF19A | Homo sapiens | Q9NV58 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RNF19A | Homo sapiens | Q9NV58 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RNF19A | Homo sapiens | Q9NV58 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ZXDC | Homo sapiens | Q2QGD7 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ZXDC | Homo sapiens | Q2QGD7 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ZXDC | Homo sapiens | Q2QGD7 | 32814053 | |
|
Intra
|
SOD1 | P00441 | FGA | Homo sapiens | Q8WW76 | 32814053 | |
|
Intra
|
SOD1 | P00441 | FGA | Homo sapiens | Q8WW76 | 32814053 | |
|
Intra
|
SOD1 | P00441 | FGA | Homo sapiens | Q8WW76 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMC4 | Homo sapiens | P43686-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMC4 | Homo sapiens | P43686-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMC4 | Homo sapiens | P43686-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RNF111 | Homo sapiens | Q6ZNA4-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RNF111 | Homo sapiens | Q6ZNA4-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RNF111 | Homo sapiens | Q6ZNA4-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SYMPK | Homo sapiens | Q92797-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SYMPK | Homo sapiens | Q92797-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SYMPK | Homo sapiens | Q92797-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | IQSEC1 | Homo sapiens | Q6DN90-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | IQSEC1 | Homo sapiens | Q6DN90-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | IQSEC1 | Homo sapiens | Q6DN90-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | LNX2 | Homo sapiens | Q8N448 | 32814053 | |
|
Intra
|
SOD1 | P00441 | LNX2 | Homo sapiens | Q8N448 | 32814053 | |
|
Intra
|
SOD1 | P00441 | LNX2 | Homo sapiens | Q8N448 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TNFAIP1 | Homo sapiens | Q13829 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TNFAIP1 | Homo sapiens | Q13829 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TNFAIP1 | Homo sapiens | Q13829 | 32814053 | |
|
Intra
|
SOD1 | P00441 | MPND | Homo sapiens | Q8N594 | 32814053 | |
|
Intra
|
SOD1 | P00441 | MPND | Homo sapiens | Q8N594 | 32814053 | |
|
Intra
|
SOD1 | P00441 | MPND | Homo sapiens | Q8N594 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ANXA8 | Homo sapiens | P13928 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ANXA8 | Homo sapiens | P13928 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ANXA8 | Homo sapiens | P13928 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RNF112 | Homo sapiens | Q9ULX5 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RNF112 | Homo sapiens | Q9ULX5 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RNF112 | Homo sapiens | Q9ULX5 | 32814053 | |
|
Intra
|
SOD1 | P00441 | OTUD7B | Homo sapiens | Q6GQQ9-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | OTUD7B | Homo sapiens | Q6GQQ9-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | OTUD7B | Homo sapiens | Q6GQQ9-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TERF2 | Homo sapiens | Q15554-4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TERF2 | Homo sapiens | Q15554-4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TERF2 | Homo sapiens | Q15554-4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | HNRNPLL | Homo sapiens | Q8WVV9-3 | 32814053 | |
|
Intra
|
SOD1 | P00441 | HNRNPLL | Homo sapiens | Q8WVV9-3 | 32814053 | |
|
Intra
|
SOD1 | P00441 | HNRNPLL | Homo sapiens | Q8WVV9-3 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CAMKK1 | Homo sapiens | Q8N5S9-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CAMKK1 | Homo sapiens | Q8N5S9-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CAMKK1 | Homo sapiens | Q8N5S9-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | KBTBD4 | Homo sapiens | Q9NVX7-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | KBTBD4 | Homo sapiens | Q9NVX7-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | KBTBD4 | Homo sapiens | Q9NVX7-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ZMAT2 | Homo sapiens | Q96NC0 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ZMAT2 | Homo sapiens | Q96NC0 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ZMAT2 | Homo sapiens | Q96NC0 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SF3B3 | Homo sapiens | Q15393 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SF3B3 | Homo sapiens | Q15393 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SF3B3 | Homo sapiens | Q15393 | 32814053 | |
|
Intra
|
SOD1 | P00441 | GPSM3 | Homo sapiens | Q9Y4H4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | GPSM3 | Homo sapiens | Q9Y4H4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | GPSM3 | Homo sapiens | Q9Y4H4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TUBB | Homo sapiens | P07437 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TUBB | Homo sapiens | P07437 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TUBB | Homo sapiens | P07437 | 32814053 | |
|
Intra
|
SOD1 | P00441 | GAPDH | Homo sapiens | P04406 | 29128334 | |
|
Intra
|
SOD1 | P00441 | RPSA | Homo sapiens | P08865 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RPSA | Homo sapiens | P08865 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RPSA | Homo sapiens | P08865 | 32814053 | |
|
Intra
|
SOD1 | P00441 | KARS1 | Homo sapiens | Q15046 | 32814053 | |
|
Intra
|
SOD1 | P00441 | KARS1 | Homo sapiens | Q15046 | 32814053 | |
|
Intra
|
SOD1 | P00441 | KARS1 | Homo sapiens | Q15046 | 32814053 | |
|
Intra
|
SOD1 | P00441 | GNB2 | Homo sapiens | P62879 | 32814053 | |
|
Intra
|
SOD1 | P00441 | GNB2 | Homo sapiens | P62879 | 32814053 | |
|
Intra
|
SOD1 | P00441 | GNB2 | Homo sapiens | P62879 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMC1 | Homo sapiens | P62191 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMC1 | Homo sapiens | P62191 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMC1 | Homo sapiens | P62191 | 29128334 | |
|
Intra
|
SOD1 | P00441 | PSMC1 | Homo sapiens | P62191 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SKIC8 | Homo sapiens | Q9GZS3 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SKIC8 | Homo sapiens | Q9GZS3 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SKIC8 | Homo sapiens | Q9GZS3 | 32814053 | |
|
Intra
|
SOD1 | P00441 | EEF1D | Homo sapiens | P29692 | 29128334 | |
|
Intra
|
SOD1 | P00441 | PSMC3 | Homo sapiens | P17980 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMC3 | Homo sapiens | P17980 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMC3 | Homo sapiens | P17980 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RPP25 | Homo sapiens | Q9BUL9 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RPP25 | Homo sapiens | Q9BUL9 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RPP25 | Homo sapiens | Q9BUL9 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMB8 | Homo sapiens | P28062-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMB8 | Homo sapiens | P28062-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PSMB8 | Homo sapiens | P28062-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | HOXC4 | Homo sapiens | P09017 | 32814053 | |
|
Intra
|
SOD1 | P00441 | HOXC4 | Homo sapiens | P09017 | 32814053 | |
|
Intra
|
SOD1 | P00441 | HOXC4 | Homo sapiens | P09017 | 32814053 | |
|
Intra
|
SOD1 | P00441 | UBB | Homo sapiens | P0CG47 | 32814053 | |
|
Intra
|
SOD1 | P00441 | UBB | Homo sapiens | P0CG47 | 32814053 | |
|
Intra
|
SOD1 | P00441 | UBB | Homo sapiens | P0CG47 | 32814053 | |
|
Intra
|
SOD1 | P00441 | MGARP | Homo sapiens | Q8TDB4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | MGARP | Homo sapiens | Q8TDB4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | MGARP | Homo sapiens | Q8TDB4 | 32814053 | |
|
Intra
|
SOD1 | P00441 | BAK1 | Homo sapiens | Q16611 | 32814053 | |
|
Intra
|
SOD1 | P00441 | BAK1 | Homo sapiens | Q16611 | 32814053 | |
|
Intra
|
SOD1 | P00441 | BAK1 | Homo sapiens | Q16611 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RBBP4 | Homo sapiens | Q09028 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RBBP4 | Homo sapiens | Q09028 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RBBP4 | Homo sapiens | Q09028 | 32814053 | |
|
Intra
|
SOD1 | P00441 | C9 | Homo sapiens | P02748 | 32814053 | |
|
Intra
|
SOD1 | P00441 | C9 | Homo sapiens | P02748 | 32814053 | |
|
Intra
|
SOD1 | P00441 | C9 | Homo sapiens | P02748 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SPATA22 | Homo sapiens | Q8NHS9 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SPATA22 | Homo sapiens | Q8NHS9 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SPATA22 | Homo sapiens | Q8NHS9 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PDZK1IP1 | Homo sapiens | Q13113 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PDZK1IP1 | Homo sapiens | Q13113 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PDZK1IP1 | Homo sapiens | Q13113 | 32814053 | |
|
Intra
|
SOD1 | P00441 | PRDX5 | Homo sapiens | P30044 | 29128334 | |
|
Intra
|
SOD1 | P00441 | PRDX5 | Homo sapiens | P30044 | 29128334 | |
|
Intra
|
SOD1 | P00441 | PRDX5 | Homo sapiens | P30044 | 29128334 | |
|
Intra
|
SOD1 | P00441 | CBLB | Homo sapiens | Q13191 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CBLB | Homo sapiens | Q13191 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CBLB | Homo sapiens | Q13191 | 32814053 | |
|
Intra
|
SOD1 | P00441 | STAC3 | Homo sapiens | Q96MF2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | STAC3 | Homo sapiens | Q96MF2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | STAC3 | Homo sapiens | Q96MF2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CRYBA2 | Homo sapiens | P53672 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CRYBA2 | Homo sapiens | P53672 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CRYBA2 | Homo sapiens | P53672 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RYBP | Homo sapiens | Q8N488 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RYBP | Homo sapiens | Q8N488 | 32814053 | |
|
Intra
|
SOD1 | P00441 | RYBP | Homo sapiens | Q8N488 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TBL1XR1 | Homo sapiens | Q9BZK7 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TBL1XR1 | Homo sapiens | Q9BZK7 | 32814053 | |
|
Intra
|
SOD1 | P00441 | TBL1XR1 | Homo sapiens | Q9BZK7 | 32814053 | |
|
Cross
|
SOD1 | P00441 | Hspa5 | Mus musculus | P20029 | 16595634 | |
|
Cross
|
SOD1 | P00441 | Hspa5 | Mus musculus | P20029 | 19171884 | |
|
Cross
|
SOD1 | P00441 | Hspa5 | Mus musculus | P20029 | 16595634 | |
|
Intra
|
SOD1 | P00441 | BCL2 | Homo sapiens | P10415 | 32814053 | |
|
Intra
|
SOD1 | P00441 | BCL2 | Homo sapiens | P10415 | 32814053 | |
|
Intra
|
SOD1 | P00441 | BCL2 | Homo sapiens | P10415 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SEM1 | Homo sapiens | P60896 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SEM1 | Homo sapiens | P60896 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SEM1 | Homo sapiens | P60896 | 32814053 | |
|
Intra
|
SOD1 | P00441 | DYNC2LI1 | Homo sapiens | Q8TCX1 | 21252941 | |
|
Intra
|
SOD1 | P00441 | CSNK1D | Homo sapiens | P48730-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CSNK1D | Homo sapiens | P48730-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | CSNK1D | Homo sapiens | P48730-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ENKUR | Homo sapiens | Q8TC29 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ENKUR | Homo sapiens | Q8TC29 | 32814053 | |
|
Intra
|
SOD1 | P00441 | ENKUR | Homo sapiens | Q8TC29 | 32814053 | |
|
Intra
|
SOD1 | P00441 | FGA | Homo sapiens | P02671-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | FGA | Homo sapiens | P02671-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | FGA | Homo sapiens | P02671-2 | 32814053 | |
|
Intra
|
SOD1 | P00441 | SNCA | Homo sapiens | P37840 | 26643113 | |
|
Intra
|
SOD1 | P00441 | SNCA | Homo sapiens | P37840 | 26643113 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 19369197 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 21257910 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 19022905 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 19022905 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 31999698 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 17592131 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 31999698 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 19022905 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 21257910 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 17592131 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 19369197 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 23831581 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 23831581 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 19022905 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 19171884 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 17592131 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 26643113 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 19022905 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 23831581 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 19828437 | |
|
Intra
|
SOD1 | P00441 | SOD1 | Homo sapiens | P00441 | 17592131 | |
|
Cross
|
SOD1 | P00441 | Chgb | Mus musculus | P16014 | 16369483 | |
|
Cross
|
SOD1 | P00441 | Chgb | Mus musculus | P16014 | 16369483 | |
|
Cross
|
SOD1 | P00441 | Chgb | Mus musculus | P16014 | 16369483 | |
|
Cross
|
SOD1 | P00441 | Chga | Mus musculus | P26339 | 16369483 |
Recombinant SOD1 Proteins
| Cat. No. | Product Name | Accession | Purity |
|---|---|---|---|
| HY-P71048 | SOD1 Protein, Human (His) | P00441 (M1-Q154) | ≥ 95%, as determined by reducing SDS-PAGE. |
SOD1 Antibodies
| Cat. No. | Product Name | Application | Reactivity |
|---|---|---|---|
| HY-P81228 | SOD-1 Antibody (YA3541) | WB, IHC-P, ICC/IF, FC | Human, Mouse, Rat |
| HY-P83888 | SOD-1 Antibody (YA3585) | WB, ICC/IF, FC, ELISA | Human, Mouse |
| HY-P83888A | SOD-1 Antibody (YA3585)(PBS only) | WB, ICC/IF, FC, ELISA | Human, Mouse |
| HY-P85373 | SOD-1 Antibody (YA5065) | WB; IHC-P; IHC-F; ICC/IF; IF-Tissue; FC | Human, Rat, Mouse |
| HY-P86424 | SOD-1 Antibody (YA6116) | WB, IHC-P, ICC/IF, IP, ELISA | Human, Mouse, Rat |
Related Diseases
| Diseases | Alias | |
|---|---|---|
| Amyotrophic Lateral Sclerosis 1 |
|
|
| Spastic Tetraplegia And Axial Hypotonia, Progressive |
|
|
| Motor Neuron Disease |
|
|
| Lateral Sclerosis |
|
|
| Eales Disease |
|
|
| Senile Cataract |
|
|
| Mild Pre-Eclampsia |
|
|
| Pneumoconiosis |
|
|
| Bronchopulmonary Dysplasia |
|
|
| Acne |
|
|
| Postcholecystectomy Syndrome |
|
|
| Spinal And Bulbar Muscular Atrophy, X-Linked 1 |
|
|
| Wilson Disease |
|
|
| Ischemia |
|
|
| Tonsillitis |
|
|
| Brain Edema |
|
|
| Myocardial Stunning |
|
|
| Amyotrophic Lateral Sclerosis 19 |
|
|
| Septooptic Dysplasia |
|
|
| Spinal Cord Neuroblastoma |
|
|
| Spinal Cord Primitive Neuroectodermal Neoplasm |
|
|
| Friedreich Ataxia |
|
|
| Methemoglobinemia |
|
|
| Down Syndrome |
|
|
| Amyotrophic Lateral Sclerosis 10 With Or Without Frontotemporal Dementia |
|
|
| Spinocerebellar Ataxia 2 |
|
|
| Hyperekplexia |
|
|
| Frontotemporal Dementia |
|
|
| Amyotrophic Lateral Sclerosis Type 6 |
|
|
| Amyotrophic Lateral Sclerosis 4, Juvenile |
|
|
| Uremia |
|
|
| Hyperhomocysteinemia |
|
|
| Retinal Vasculitis |
|
|
| Amyotrophic Lateral Sclerosis 2, Juvenile |
|
|
| Hyperglycemia |
|
|
| Amyotrophic Lateral Sclerosis 20 |
|
|
| Vascular Disease |
|
|
| Charcot-Marie-Tooth Disease, Axonal, Type 2e |
|
|
| Progressive Muscular Atrophy |
|
|
| Amyotrophic Lateral Sclerosis 8 |
|
|
| Progressive Bulbar Palsy |
|
|
| Pancreatitis |
|
|
| Menkes Disease |
|
|
| Keratoconus |
|
|
| Varicocele |
|
|
| Erysipelas |
|
|
| Frontotemporal Dementia And/Or Amyotrophic Lateral Sclerosis 4 |
|
|
| Pre-Eclampsia |
|
|
| Porphyria, Acute Intermittent |
|
|
| Acute Pancreatitis |
|
|
| Lung Disease |
|
|
| Exfoliation Syndrome |
|
|
| Atrophic Gastritis |
|
|
| Amyotrophic Lateral Sclerosis 11 |
|
|
| Parkinson Disease, Late-Onset |
|
|
| Locked-In Syndrome |
|
|
| Frontotemporal Dementia And/Or Amyotrophic Lateral Sclerosis 1 |
|
|
| Bacterial Meningitis |
|
|
| Amyotrophic Lateral Sclerosis 18 |
|
|
| Male Infertility |
|
|
| Creutzfeldt-Jakob Disease |
|
|
| Amyotrophic Lateral Sclerosis 16, Juvenile |
|
|
| Amyotrophic Lateral Sclerosis Type 12 |
|
|
| Amyotrophic Lateral Sclerosis-Parkinsonism/Dementia Complex 1 |
|
|
| Maple Syrup Urine Disease |
|
|
| Tetanus |
|
|
| Cataract |
|
|
| Diabetes Mellitus |
|
|
| Spinal Muscular Atrophy |
|
|
| Chronic Granulomatous Disease |
|
|
| Type 2 Diabetes Mellitus |
|
|
| Peyronie Disease |
|
|
| Amyotrophic Lateral Sclerosis Type 15 |
|
|
| Amyotrophic Lateral Sclerosis 21 |
|
|
| Hypotonia |
|
|
| Constipation |
|
|
| Postpoliomyelitis Syndrome |
|
|
| Viral Hepatitis |
|
|
| Dementia |
|
|
| Platelet Aggregation, Spontaneous |
|
|
| Pseudobulbar Palsy |
|
|
| Alzheimer Disease, Familial, 1 |
|
|
| Beta-Thalassemia |
|
|
| Amyotrophic Lateral Sclerosis Type 14 |
|
|
| Glycogen Storage Disease |
|
|
| Shigellosis |
|
|
| Fatal Familial Insomnia |
|
|
| Toxic Encephalopathy |
|
|
| Chromosomal Duplication Syndrome |
|
|
| Cardiovascular System Disease |
|
|
| Huntington Disease |
|
|
| Cerebral Palsy |
|
|
| Hypertension, Essential |
|
|
| Short Syndrome |
|
|
| Cataract 23, Multiple Types |
|
|
| Heart Disease |
|
|
| Pancreatic Colloid Cystadenoma |
|
|
| Chronic Wasting Disease |
|
|
| Anthracosis |
|
|
| Microvascular Complications Of Diabetes 5 |
|
|
| Inclusion Body Myopathy With Paget Disease Of Bone And Frontotemporal Dementia |
|
|
| Chronic Kidney Disease |
|
|
| Autism Spectrum Disorder |
|
|
| Malaria |
|
|
| Dementia, Lewy Body |
|
|
| Pick Disease Of Brain |
|
|
| Neuroblastoma |
|
|
| Pheochromocytoma |
|
|
| Hereditary Ataxia |
|
|
| Autosomal Dominant Cerebellar Ataxia |
|
|
| Spastic Paraplegia 38, Autosomal Dominant |
|
|
| Supranuclear Palsy, Progressive, 1 |
|
|
| Tetralogy Of Fallot |
|
|
| Cerebellar Disease |
|
|
| Alzheimer Disease 9 |
|
|
| Neuromuscular Disease |
|
|
| Scoliosis |
|
|
| Spinal Muscular Atrophy, Type I |
|
|
| Autism |
|
|
| Movement Disease |
|
|
| Giant Axonal Neuropathy 2 |
|
|
| Choreatic Disease |
|
|
| Schizophrenia |
|
|
| Hereditary Spastic Paraplegia |
|
|
| Respiratory Failure |
|
|
| Peripheral Nervous System Disease |
|
|
| Neuronal Ceroid Lipofuscinosis |
|
|
| Nervous System Disease |
|
|
| Charcot-Marie-Tooth Disease |
|
|
| Myopathy |
|
|
| Retinitis Pigmentosa |
|
|
Orthologs Information
| Species | Symbol | Source | ID |
|---|---|---|---|
| Canis familiaris | SOD1 | VGNC | VGNC:46653 |
| Rattus norvegicus | SOD1 | RGD | RGD:3731 |
| Macaca mulatta | SOD1 | VGNC | VGNC:77687 |
| Mus musculus | SOD1 | MGD | MGI:98351 |
| Others | SOD1 | NCBI |